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!!Paolo Bernardi
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1. __Bernardi, P.__ (__1992__) Modulation of the Mitochondrial Cyclosporin A-Sensitive Permeability Transition Pore by the Proton Electrochemical Gradient. Evidence that the Pore can be Opened by Membrane Depolarization. ''J Biol Chem'' 267, 8834-8839 - __261 citations (ISI) __
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2. Petronilli, V., Costantini, P., Scorrano, L., Colonna, R., Passamonti, S. and __Bernardi, P__. (__1994__) The Voltage Sensor ofthe Mitochondrial Permeability Transition Pore is Tuned by the Oxidation-Reduction State of Vicinal Thiols. Increase ofthe Gating Potential by Oxidants and its Reversal by Reducing Agents. ''J Biol Chem'' 269, 1663 8-16642 - __338 citations (ISI)__
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3. Nicolli, A., Basso, E., Petronilli, V., Wenger, R.M. and __Bernardi, P.__ (__1996__) Interactions of Cyclophilin with the Mitochondrial Inner Membrane and Regulation of the Permeability Transition Pore, a Cyclosporin A-sensitive Channel. ''J Biol Chem'' 271, 2185-2192 – __268 citations (ISI)__
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4. Costantini, P., Chernyak, B.V., Petronilli, V. and __Bernardi, P__. (__1996__) Modulation of the Mitochondrial Permeability Transition Pore by Pyridine Nucleotides and Dithiol Oxidation at Two Separate Sites. ''J Biol Chem'' 271, 6746-675l - __263 citations (ISI)__
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5. __Bernardi, P.__ (__1999__) Mitochondrial Transport of Cations: Channels, Exchangers and Permeability Transition. ''Physiol Rev'' 79, 1127-1155 - __659 citations (ISI)__
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6. Irwin, W., Bergamin, N., Sabatelli, P., Reggiani, C., Megighian, A., Merlini, L., Braghetta, P., Volpin, D., Bressan, G.M., __Bernardi, P.__*, and Bonaldo, P.* (__2003__) Mitochondrial dysfunction and apoptosis in rnyopathic mice with collagen VI deficiency, ''Nat Genet'' 35, 367-371 *Corresponding Authors [[Covered in News and Views by Rizzuto (2003) Nat. Genet. 35, 300 and in an Editorial by Olsen ''Matrix Biology'' (2003) 22, 519] __- 98 citations (ISI)__
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7. Basso, E., Fante, L., Fowlkes, J., Petronilli, V. Forte, M.A. and __Bernardi, P.__ (__2005__) Properties of the Permeability Transition Pore in Mitochondria Devoid of Cyclophilin D, ''J Biol Chem'' 280, l8558-18561 [[19%%sup th/% most read article in the ''Journal of Biological Chemistry'' in May, 2005; reviewed with top score (6, must read) in Faculg of 1000 Biology; commented upon by A. Gawrylewski, ''The Scientist'' (2007) 21, 73] - __182 citations (ISI)__
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8. Angelin, A., Tiepolo, T., Sabatelli, P., Grumati, P., Bergamin, N., Goliieri, C., Mattioli, E., Gualandi, F., Ferlini, A., Merlini, L., Maraldi, N.M., Bonaldo, P. and __Bernardi, P__. (__2007__) Mitochondrial dysfunction in the pathogenesis of Ullrich congenital muscular dystrophy and prospective therapy with cyclosporins, ''Proc Natl Acad Sci USA'' 104, 99l-996 [[covered in an Editorial by Olsen, ''Matrix Biology'' (2007) 26, 145; reviewed (score 3, recommended) in Faculty of 1000 Medicine] - __41 citations (ISI)__
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9. Merlini, L., Angelin, A., Tiepolo, T., Braghetta, P., Sabatelli, P., Zarnparelli, A., Ferlini, A., Maraldi, N.M., Bonaldo, P. and __Bernardi, P.__ (__2008__) Cyclosporin A corrects mitochondrial dysfunction and muscle apoptosis in patients with collagen VI myopathies, ''Proc Natl Acad Sci USA'' 105, 5225-5229 [[covered in an Editorial by Olsen, ''Matrix Biology'' (2008) 27 273; reviewed by Robinson, Neurology Today, Nov 20, 2008, 22-23 and Kaplan (2008) ''Med. Sci.'' (Paris) 24, 470] - __37 citations (ISI)__
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l0. Giorgio, V., Bisetto, E., Soriano, M.E., Dabbeni-Sala, F., Basso, E., Petronilli, V., Forte, M.A., __Bernardi, P.__* and Lippe, G.* (__2009__) Cyclophilin D modulates mitochondrial FGF) ATP synthase by interacting with the lateral stalk of the complex, *Corresponding authors, __J Biol Chem__ 284, 33982-33988 [[reviewed with top score (6, must read) in Faculty of 1000 Biology]


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